Brain and spinal cord (CNS) tumors are a common cancer in childhood, and they are a significant cause of morbidity. Early recognition of symptoms, prompt diagnosis, and timely treatment are associated with improved outcomes. In children, the most common CNS tumors are gliomas, embryonal tumors, and germ cell tumors. Other CNS tumor types of notes in children include pituitary tumors, choroid plexus tumors, craniopharyngiomas, dysembryoplastic neuroepithelial tumors, and meningiomas. Risk factors for childhood tumors include genetic links and ionizing radiation exposure. Presenting symptoms are age-specific and site-specific A combined, multidisciplinary approach to managing these patients is essential. It is unusual for a single modality to be sufficient for cure. Survivors of brain tumors in childhood have complex health and social care needs which may persist for many decades.